Unusual location and orientation of crossed fused kidneys in a patient with history of repaired congenital diaphragmatic hernia and hypoplastic lung: Importance of [99mTc]Tc-DMSA SPECT/CT and correlation with diuretic renal scan and VCUG

Document Type : Case Report

Authors

1 Nuclear Medicine Research Center, Mashhad University of Medical Sciences, Mashhad, Iran

2 Nephrology Research Center, Mashhad University of Medical Sciences, Mashhad, Iran

3 Department of Radiology, Mashhad University of Medical Sciences, Mashhad, Iran

Abstract

 We presented a 2.5-year-old boy with a history of the left pulmonary hypoplasia, repaired congenital diaphragmatic hernia and multiple episodes of pyelonephritis was referred to our department for [99mTc]Tc-DMSA and [99mTc]Tc-EC renal scintigraphy. The scans revealed an unusual pattern of renal uptake with horizontally aligned kidneys located high on left lower thoracic region extended to the mid abdomen. SPECT/CT of the [99mTc]Tc-DMSA scan clearly demonstrated the unusual location of the kidneys which was due to crossed fused renal ectopia and elevated diaphragm. Diuretic renal scans showed no evidence of renal obstruction. Additionally, the VCUG scan indicated vesicoureteral reflux in both ureters.

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References

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